Actelion has published a new cookie policy. This policy provides information about what cookies are and gives details of those deployed on this site.

By closing this message, you consent to our use of cookies on this site in accordance with Actelion's cookies policy unless you want to find out how to manage cookies.
A  B  C  D  E  F  G  H  I  J  K  L  M  N  O  P  Q  R  S  T  U  V  W  X  Y  Z 

The definition of Pulmonary arterial hypertension (PAH)

A disorder primarily of small pulmonary arteries which results in a progressive rise in pulmonary vascular resistance and right ventricular failure. There are several forms of PAH including Idiopathic Pulmonary Arterial Hypertension (IPAH) and Associated PAH related to a range of disease processes, including connective tissue disease, congenital heart disease, HIV infection and sickle-cell disease. For the haemodynamic definition, please refer to the website.

If there are any questions about these definitions or how to apply them, please contact your PAH centre or specialist.